General anaesthesia in an adult patient with Morquio syndrome with emphasis on airway issues

  • Lajla Kadić Department of Anesthesiology, Radboud University Nijmegen Medical Centre
  • Jacques J. Driessen Department of Anesthesiology, Radboud University Nijmegen Medical Centre
Keywords: Morquio syndrome, mucopolysaccharidosis, neck instability, general anesthesia, fiberoptic intubation

Abstract

Patients with Morquio syndrome possess a number of characteristics which may complicate an anaesthetic procedure. The most important is that a deposition of mucopolysaccharides in the soft tissues of the oro-pharynx distorts the airway, making the airway management difficult, while the atlanto-axial instability puts these patients at risk of subluxation and quadriparesis.

As the endotracheal intubation in Morquio syndrome patients may be difficult or even impossible, we recommend the technique of awake fiberoptic intubation to be considered.

Our approach to awake fiberoptic intubation in an adult patient is described in this case report.

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General anaesthesia in an adult patient with Morquio syndrome with emphasis on airway issues
Published
2012-05-20
How to Cite
1.
Kadić L, J. Driessen J. General anaesthesia in an adult patient with Morquio syndrome with emphasis on airway issues. Bosn J of Basic Med Sci [Internet]. 2012May20 [cited 2020Oct.31];12(2):130-3. Available from: https://www.bjbms.org/ojs/index.php/bjbms/article/view/2513
Section
Case reports